Abstract

Somatosensory evoked potentials (SEPs) were recorded in a group of 21 patients with dystrophia myotonica and in a group of controls. Those with dystrophia myotonica had longer absolute peak latencies due to slower peripheral conduction. SEP abnormalities revealed peripheral and/or central conduction delays in 33% of the dystrophia myotonica subjects. There was no apparent relationship between the clinical severity of the disease and SEP abnormality.