You are here

Article Text

Article menu
Download PDFPDF
Letters to the editor
Vocal cord abductor paralysis in spinocerebellar ataxia type 1
  1. T SHIOJIRI,
  2. T TSUNEMI,
  3. T MATSUNAGA
  1. Department of Neurology, Asahi General Hospital, Chiba, Japan
  2. Department of Neurology
  3. Department of Oto-Rhino-Laryngology, Hokkaido University School of Medicine, Hokkaido, Japan
  4. Department of Neurology, Tokyo Metropolitan Neurological Hospital, Tokyo, Japan
  5. Department of Neurology
  6. Tokyo Medical and Dental University, Tokyo, Japan
  1. Dr Toshiaki Shiojiri, Department of Neurology, Asahi General Hospital, I-1345, Asahi-city, Chiba 289–2511, Japan. Telephone 0081 479 63 8111; fax 0081 479 60 1210.
  1. H SASAKI,
  2. I YABE,
  3. K TASHIRO
  1. Department of Neurology, Asahi General Hospital, Chiba, Japan
  2. Department of Neurology
  3. Department of Oto-Rhino-Laryngology, Hokkaido University School of Medicine, Hokkaido, Japan
  4. Department of Neurology, Tokyo Metropolitan Neurological Hospital, Tokyo, Japan
  5. Department of Neurology
  6. Tokyo Medical and Dental University, Tokyo, Japan
  1. Dr Toshiaki Shiojiri, Department of Neurology, Asahi General Hospital, I-1345, Asahi-city, Chiba 289–2511, Japan. Telephone 0081 479 63 8111; fax 0081 479 60 1210.
  1. N NISHIZAWA
  1. Department of Neurology, Asahi General Hospital, Chiba, Japan
  2. Department of Neurology
  3. Department of Oto-Rhino-Laryngology, Hokkaido University School of Medicine, Hokkaido, Japan
  4. Department of Neurology, Tokyo Metropolitan Neurological Hospital, Tokyo, Japan
  5. Department of Neurology
  6. Tokyo Medical and Dental University, Tokyo, Japan
  1. Dr Toshiaki Shiojiri, Department of Neurology, Asahi General Hospital, I-1345, Asahi-city, Chiba 289–2511, Japan. Telephone 0081 479 63 8111; fax 0081 479 60 1210.
  1. K TAKAMOTO
  1. Department of Neurology, Asahi General Hospital, Chiba, Japan
  2. Department of Neurology
  3. Department of Oto-Rhino-Laryngology, Hokkaido University School of Medicine, Hokkaido, Japan
  4. Department of Neurology, Tokyo Metropolitan Neurological Hospital, Tokyo, Japan
  5. Department of Neurology
  6. Tokyo Medical and Dental University, Tokyo, Japan
  1. Dr Toshiaki Shiojiri, Department of Neurology, Asahi General Hospital, I-1345, Asahi-city, Chiba 289–2511, Japan. Telephone 0081 479 63 8111; fax 0081 479 60 1210.
  1. T YOKOTA,
  2. H MIZUSAWA
  1. Department of Neurology, Asahi General Hospital, Chiba, Japan
  2. Department of Neurology
  3. Department of Oto-Rhino-Laryngology, Hokkaido University School of Medicine, Hokkaido, Japan
  4. Department of Neurology, Tokyo Metropolitan Neurological Hospital, Tokyo, Japan
  5. Department of Neurology
  6. Tokyo Medical and Dental University, Tokyo, Japan
  1. Dr Toshiaki Shiojiri, Department of Neurology, Asahi General Hospital, I-1345, Asahi-city, Chiba 289–2511, Japan. Telephone 0081 479 63 8111; fax 0081 479 60 1210.

https://doi.org/10.1136/jnnp.67.5.695

Statistics from Altmetric.com

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    Vocal cord abductor paralysis (VCAP) is considered a sign of a poor prognosis in neurodegenerative diseases, because severe laryngeal dysfunction by VCAP may result in acute airway obstruction and require emergency tracheotomy.1

    Although VCAP is a cardinal feature in multiple system atrophy (MSA), it has not been reported in several types of spinocerebellar ataxia with dominant inheritance. We evaluated the movements of the vocal cords of seven patients with SCA1 by laryngofibroscopy.

    Seven unrelated patients with SCA1 who had the expanded CAG repeat of ataxin-1 were investigated. There were two men and five women ranging in age from 27 to 67 years old (mean 44.5 years). Spouses and other family members, in addition to the patients, were questioned about events of stridor, dyspnoea, and dysphagia. Vocal cord movement was examined by laryngofibroscopy and recorded during inspiration and phonation. The rating scale used to evaluate maximal abduction of the vocal …

    View Full Text