J Neurol Neurosurg Psychiatry 69:124-126 doi:10.1136/jnnp.69.1.124
  • Short report

Arnold-Chiari malformation and nystagmus of skew

  1. Christina Pieha,
  2. Irene Gottlobb
  1. aDepartment of Strabismus and Neuroophthalmology, Kantonsspital StGallen, Switzerland, bDepartment of Ophthalmology, University of Leicester, UK
  1. Professor Irene Gottlob, Leicester Royal Infirmary, Department of Ophthalmology, LE1 5WW Leicester, UKig15{at}
  • Received 20 October 1999
  • Revised 28 February 2000
  • Accepted 6 March 2000


The Arnold-Chiari malfomation is typically associated with downbeat nystagmus. Eye movement recordings in two patients with Arnold-Chiari malfomation type 1 showed, in addition to downbeat and gaze evoked nystagmus, intermittent nystagmus of skew. To date this finding has not been reported in association with Arnold-Chiari malfomation. Nystagmus of skew should raise the suspicion of Arnold-Chiari malfomation and prompt sagittal head MRI examination.


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