Arnold-Chiari malformation and nystagmus of skew
- aDepartment of Strabismus and Neuroophthalmology, Kantonsspital StGallen, Switzerland, bDepartment of Ophthalmology, University of Leicester, UK
- Professor Irene Gottlob, Leicester Royal Infirmary, Department of Ophthalmology, LE1 5WW Leicester, UK
- Received 20 October 1999
- Revised 28 February 2000
- Accepted 6 March 2000
The Arnold-Chiari malfomation is typically associated with downbeat nystagmus. Eye movement recordings in two patients with Arnold-Chiari malfomation type 1 showed, in addition to downbeat and gaze evoked nystagmus, intermittent nystagmus of skew. To date this finding has not been reported in association with Arnold-Chiari malfomation. Nystagmus of skew should raise the suspicion of Arnold-Chiari malfomation and prompt sagittal head MRI examination.