PT  - JOURNAL ARTICLE
AU  - D A Grimes
AU  - A E Lang
AU  - C Bergeron
TI  - Late adult onset chorea with typical pathology of Hallervorden-Spatz syndrome
AID  - 10.1136/jnnp.69.3.392
DP  - 2000 Sep 01
TA  - Journal of Neurology, Neurosurgery & Psychiatry
PG  - 392--395
VI  - 69
IP  - 3
4099  - http://jnnp.bmj.com/content/69/3/392.short
4100  - http://jnnp.bmj.com/content/69/3/392.full
SO  - J Neurol Neurosurg Psychiatry2000 Sep 01; 69
AB  - Senile chorea is a well recognised but poorly understood clinical entity characterised by a slowly progressive, generalised chorea in elderly people without mental deterioration or a clear underlying cause. The Hallervorden-Spatz syndrome is typically thought of as a paediatric condition with extrapyramidal features and dementia. However, it has been described in adults usually presenting with parkinsonism plus dementia. An elderly woman with slowly progressive chorea without dementia was found at postmortem to have the pathological features originally described by Hallervorden and Spatz. This association has not previously been reported.