Summary of the variables scored and the method of scoring in the six subtests of the myoclonus rating scale21 25
| Score | |
|---|---|
| (A) Stimulus sensitivity: | |
| Stimuli: tendon tap to finger or toe, pinprick, loud noise, flash of bright light, visual threat | 0–40 |
| Range 0–8 for each of these 5 stimuli | |
| (B) Motor impairment: | 0–96 |
| Spontaneous myoclonus: 0–32 (score 0–4 for each of 8 areas) | |
| Action myoclonus frequency: 0–32 (score 0–4 for stereotyped movement in each of 8 areas) | |
| Action myoclonus severity: 0–32 (score 0–4 according to degree of interference with function) | |
| (C) Functional disability: | 0–28 |
| Score 0-4 for degree of impairment of speech, swallowing, eating (knife and fork), washing, dressing, walking, handwriting | |
| (D) Handwriting: | 0–10 |
| Signing name 0–5; copying 0–5 | |
| (E) Global assessment by investigator: | 0–4 |
| Score 0–4 for from none to severe | |
| (F) Global assessment by patient: | 0–10 |
| Score 0–10 using 10 cm visual analogue scale | |
| Adjusted sum score (A/40 + B/96 + C/28 + D/10 + E/4 + F/10) x 10/6) | 0–10 |
Type, frequency, and severity of myoclonus evaluated with scoring for stimulus sensitivity and motor impairment were assessed in eight body areas: eyes, face, neck, trunk, right and left arm, right and left leg.