Table 1

Demographic data

PatientsP1P2P3P4P5P6P7
Age/sex44/M37/M40/F65/M60/M47/F41/M
Duration (months)10251412601019
ProgressionStepwiseProgressiveProgressiveProgressiveStepwiseStepwiseStepwise
WeaknessUpper limbsUpper limbsUpper limbUpper limbUpper limbsUpper+lower limbsUpper limb
LocationBilateralBilateralRightRightBilateralRightLeft
Distal+proximalDistalDistalDistalDistalDistalDistal
AtrophyNoneHandsNoneNoneHandNoneHands (bilateral)
LocationBilateralLeftForearm (left)
AntiGM1 titre3200NDNDND800800800
CTxNoYesNoNoNoNoYes
  • Duration=time elapsed between onset of symptoms and diagnosis; ND=Not detected; Ctx=cyclophosphamide.