Patient | Diagnosis | Sex | Age | EDS | NSD | BMI |
---|---|---|---|---|---|---|
1 | MD 1 | M | 37 | Y | Y | 24.0 |
2 | MD 2 | M | 33 | Y | Y | 22.0 |
3 | MD 3 | M | 29 | Y | Y | 21.0 |
4 | MD 4 | M | 41 | Y | Y | 21.5 |
5 | MD 5 | M | 43 | Y | Y | 22.0 |
6 | MD 6 | M | 36 | Y | Y | 23.0 |
7 | Vasc myop | F | 32 | Y | N | 22.0 |
8 | Mito myop | F | 44 | Y | Y | 26.0 |
9 | Mito myop | F | 37 | Y | Y | 23.0 |
10 | Gly sto dz | M | 32 | Y | N | 24.5 |
11 | Gly sto dz | M | 28 | Y | Y | 22.0 |
12 | Limb gir MD | F | 17 | Y | Y | 23.5 |
13 | Duchenne MD | M | 12 | Y | N | 18.0 |
14 | Duchenne MD | M | 14 | Y | N | 20.0 |
15 | Duchenne MD | M | 14 | Y | Y | 19.0 |
16 | Myo unclass | F | 43 | Y | Y | 27.0 |
17 | Post tr phrenic | M | 51 | Y | Y | 26.0 |
18 | Post tr bulbar | M | 24 | Y | Y | 23.0 |
19 | Syringomyelia | M | 39 | Y | Y | 21.0 |
20 | Slow SCD | M | 49 | Y | Y | 23.0 |
Mean | — | — | 32.75 | — | — | 22.58 |
SD | — | — | 11.66 | — | — | 2.27 |
BMI=body mass index (kg/m2); EDS=excessive daytime sleepiness; NSD=nocturnal sleep disruption (Y=yes, N=no); MD=myotonic dystrophy; Vasc myop=vascular myopathy; Mitoch myop=mitochondrial myopathy; Glyc sto dz=glycogen storage disease; Limb gir MD=limb girdle dystrophy; Post tr phrenic=post-traumatic phrenic nerve paralysis; Post tr bulbar=post-traumatic bulbar lesion; Slow SCD=slow evolving spinocerebellar degeneration.