Electrophysiological data from the six patients

		C2-1	C2-2	C12	C64	C10	C13	Normal
MNC:
Median	Ampl (mV)	4	0.8	0.6	0.8	1.0	0.2
	DL (ms)	4.6	4.4	6.6	5.7	4.8	8.6
	CV (m/s)	36	33	29	31	29	21
Peroneal	Ampl (mV)	2.5	0.4	NE	NE	NE	NE
	DL (ms)	7.4	5.1	NE	NE	NE	NE
	CV (m/s)	38	30	NE	NE	NE	NE
SNC:
Sural	Ampl (mV)	2	4	NE	0.5	NE	NE
	DL (ms)	3.6	2.9	NE	8.1	NE	NE
	CV (m/s)	31	31	NE	22	NE	NE
BAERs:
Right	I (ms)	1.58	2.20	1.82	1.68	1.52	1.41	<1.73
	III (ms)	4.54	4.58	4.63	4.61	3.12	2.89	<3.79
	V (ms)	6.14	7.22	6.87	6.24	5.25	4.97	<5.72
Left	I (ms)	1.72	1.62	1.98	1.85	1.43	1.51	<1.73
	III (ms)	4.24	4.60	4.75	4.79	2.98	3.13	<3.79
	V (ms)	6.20	6.22	7.31	6.87	4.95	4.87	<5.72
VEPs:
Right	Lat (ms)	111.5	95.5	NP	112.2	NP	NP	80–108
Left	Lat (ms)	97	110	NP	110.8	NP	NP	R-L<8

MNC=Motor nerve conduction; Ampl=amplitude; DL=distal latency; CV=conduction velocity; SNC=sensory nerve conduction, BAERs=brain stem auditory evoked responses: waves I, III, and V; VEPs=visual evoked potentials; Lat=latency; NE=not evoked; NP=not performed.