Average risk per decade of patients presenting with vestibular schwannoma having NF2
| Age (y) | % with NF2 | % with NF2 UVS at diagnosis | % with NF2 with no FH and no other NF2 features |
|---|---|---|---|
| 10–19 | 33% (22–50%) | 6% (2.6–9%) | 1% (0.3–1.4%) |
| 20–29 | 15% (8–22%) | 2.7% (0.9–4%) | 0.45% (0.1–0.6%) |
| 30–39 | 5% (3–8%) | 0.9% (0.3–1.4%) | 0.15% (0.03–2.2%) |
| 40–49 | 2% (1–3%) | 0.36% (0.1–0.54%) | 0.06% (0.01–0.08%) |
| 50–59 | 1% (0.5–1.5%) | 0.18% (0.06–0.27%) | 0.03% (0.007–0.05%) |
| 60–69 | — | — | — |
UVS= unilateral vestibular schwannoma; FH=family history.