Patient | Age at death | Sex | Onset to death (y) | Motor/ Sensory symptoms | Modified Rankin score (pretreatment) | Therapeutic response | Muscle | Modified Rankin score (before death) | CSF protein (mg/dl) | Cause of death | |||||||||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Cortico-steroid | Plasma-phoresis | IVIg | Atrophy | Weakness | |||||||||||||||||||
1 | 72 | M | 3.5 | M>S | 4 | + | + | 2 | 3 | 5 | 105 | Heart failure | |||||||||||
2 | 55 | F | 0.8 | M>S | 3 | + | 2 | 3 | 5 | 800 | Cardiovascular disease | ||||||||||||
3 | 49 | M | 8 | M>S | 3 | − | 3 | 3 | 4 | 99 | Pneumonia | ||||||||||||
4 | 68 | M | 3 | M=S | 3 | + | 2 | 2 | 3 | 218 | Pneumonia | ||||||||||||
5 | 54 | F | 0.3 | M=S | 5 | + | 1 | 3 | 5 | 171 | Pneumonia | ||||||||||||
6 | 57 | M | 2.5 | M>S | 3 | + | + | 2 | 3 | 5 | 110 | Endocarditis | |||||||||||
7 | 70 | F | 1 | M>S | 3 | + | 1 | 1 | 2 | 73 | Cardiovascular disease | ||||||||||||
8 | 73 | M | 0.5 | M=S | 5 | + | 1 | 3 | 4 | 128 | Pneumonia | ||||||||||||
9 | 64 | M | 15 | M<S | 2 | + | 1 | 1 | 2 | NA | Bronchitis/ Meningitis |
Modified Rankin score: 0=asymptomatic; 1=non-disabling symptoms that do not interfere with lifestyle; 2=minor disability symptoms that lead to some restriction of lifestyle but do not interfere with the patients’ capacity to look after themselves; 3=moderate disability symptoms that significantly interfere with lifestyle or prevent totally independent existence; 4 = moderately severe disability symptoms that clearly prevent independent existence, although patient does not need constant attention day and night; and 5=severely disabled, totally dependent requiring constant attention day and night.10Modified Rankin scores of some patients were assessed on the clinical records. Therapeutic response was evaluated as positive if the modified Rankin score improved one grade or more. Muscle atrophy and weakness were respectively assessed as 1, 2, and 3 denoting mild, moderate, and severe degrees. NA=not available. The grading was made within 3 months before death.