Lentiform nucleus | Caudate nucleus | Thalamus | Substantia nigra | |
---|---|---|---|---|
Dystonia10 2-150 | 49/86 (57%) | 13/86 (15%) | 8/86 (9%) | NI |
Torticollis14 | 7/10 (70%) | 1/10 (10%) | NI | NI. |
Parkinson’s disease9 | NI | NI | NI | 17/30 (57%) |
Huntington’s disease (present study) | 3/45 (6%) | 6/45 (13%) | 0/45 (0%) | 12/45 (27%) |
↵2-150 Idiopathic dystonia/cervical dystonia (n=43), upper limb dystonia (n=12), facial dystonia (n=16), generalised dystonia (n=2), tardive dystonia/cervical dystonia (n=7), tardive facial dystonia (n=3), dopa responsive dystonia(n=2), kinesiogenic dystonia (n=1); NI=not indicated.