Table 1

Clinical features of patients

NoSexAge (y)DM type/
duration (y)/
HbA1C (%)
PainSensory Sx/
duration (months)
Motor Sx/
duration (months)
Trunk/vertex sensory lossAutonomic SxHypertension/ kidney/retinaWeight loss (kg)CSF Protein (mg/dl)
1F42I/20/8.5NoLE/24LE>UE/12No/NoCV, GI, PYes/Yes/Yes584
asymmetric
2M52II/14/8.7NoLE>UE/6LE>UE/3Yes/NoNo/No/Yes10170
asymmteric
3M53I/16/7.3LBUE>LE/24LE>UE/4Yes/YesCV, GI, P, SYes /Yes/Yes1476
asymmetric
4M59II/10/8.7NoLE+UE/12LE+UE+R/2Yes/YesCV, GI, P, SYes/Yes/No1042
symmetric
5F60I/5/7.5LBUE>LE/6LE>UE/3No/NoCVYes/Yes/Yes956
asymmetric
6M60II/10/8.3LBLE/4LE>UE/6No/NoGINo/No/No10135
symmetric
7F66II/2/8.9LELE/5LE/4No/NoCV, PNo/No/No2571
asymmetric
8F71II/18/9.8LB, LELE/12LE>UE/2Yes/YesNo/No/No590
symmetric
9M71II/10/7.9LELE/12LE+UE+R/5Yes/NoCV, SYes/No/No14125
asymmetric
10M49II/4/7.0LB, LELE/24LE+UE+F/18Yes/NoCV, GI, P, SNo/Yes/No19176
symmetric
11F42I/36/10.4LBLE/12LE+UE+F/7Yes/YesCV, GI, PNo/Yes/Yes9128
symmetric
12M66II/5/8.3LBLE/6LE>UE/4Yes/NoCV, GINo/No/No1253
symmetric
13F72II/4/8.1LB, UELE+UE/9LE+UE/4Yes/NoNo/No/No1373
asymmetric
14M66II/4/8.7LB, LELE/5LE>UE/5Yes/NoCV, GI, SNo/Yes/No10150
asymmetric
15M68II/10/8.6LB, LELE/4LE>UE/3No/NoCV, SYes/No/No9140
symmetric
  • Sx=Symptoms and signs; LE/UE=lower/upper extremities; F=face; R=respiratory; LB=low back; CV=cardiovascular; P=pupils; GI=gastrointestinal; S=abnormal sweating