Patient No | Age at onset | Main clinical features | Other clinical features | MRI | Possible diagnosis |
H5 | 64 | Chorea, dementia, depression | Corticosubcortical atrophy | HD-like | |
H48 | 47 | Chorea, dementia, behav disturb | Obsessive features | Caudate atrophy | HD-like |
H100 | 62 | Chorea, dementia | Frontal release signs | Corticosubcortical atrophy | HD-like |
H102 | 66 | Chorea, dementia | Frontal release signs | Lentiform nucleus atrophy | HD-like |
Corticosubcortical atrophy, | |||||
H122 | 56 | Chorea, dementia, depression | pallidal hyperintensities | HD-like | |
H154 | 40 | Chorea, dementia, depression | Frontal release signs | ND | HD-like |
Behav disturb | |||||
H26 | 60 | Chorea, dementia, behav disturb | Ataxia | Cerebellar and caudal atrophy | HD-like/cerebellar disorder |
H139 | 30 | Choreaoathetosis, dysarthria, | Pyramidal signs, hypertension, | ND | HD-like |
dementia, behav disturb. | Angor, ischaemic cardiopathy | ||||
H150 | 64 | Chorea, dementia, behav disturb | Cortical and cerebellar atrophy | HD-like/cerebellar disorder | |
H155 | 46 | Chorea, dementia, behav disturb | Ataxia | Cortical and cerebellar atrophy | HD-like/cerebellar disorder |
H165 | 49 | Chorea, dementia | Ataxia | HD-like/cerebellar disorder |
behav disturb=Behavioural disturbances; ND=not determined.