No | Sex | Age | Site of lesion | Pain | Increase in size | Neurological deficit (sensory and motor impairment) |
1 | F | 49 | Prevertebral at L1 | Yes | Not visible1-150 | Yes |
2 | M | 37 | Pelvis | Yes | Not visible1-150 | No |
3 | F | 19 | L brachial plexus | Yes | Not visible1-150 | Yes |
4 | F | 23 | L thigh | Yes | Yes | Yes |
R lower limb | Yes | Yes | No | |||
5 | F | 41 | L thigh | Yes | Yes | No |
L axilla | Yes | Yes | No | |||
6 | M | 62 | R thigh | Yes | Yes | Yes |
7 | M | 22 | L thigh (medial) | Yes | Yes | Yes |
L thigh (post.) | Yes | Yes | Yes | |||
8 | F | 26 | L supraclavicular fossa | Yes | Yes | Yes |
9 | F | 35 | L buttock | Yes | Yes | No |
10 | F | 34 | R lower limb | Yes | Yes | No |
11 | F | 12 | R thigh | No | Yes | No |
12 | F | 27 | L popliteal fossa | Yes | Yes | Yes |
13 | M | 14 | R cervical region | Yes | Yes | No |
14 | M | 24 | Pelvis | No | Yes | Yes |
15 | M | 14 | L popliteal fossa | Yes | Yes | Yes |
16 | M | 26 | Retroperitoneum, | No | not visible1-150 | Yes |
R popliteal fossa | No | Yes | Yes | |||
L popliteal fossa | No | Yes | Yes | |||
17 | F | 22 | L upper limb | Yes | Yes | No |
18 | M | 15 | R lower limb | No | Yes | Yes |
↵1-150 Indicates plexiform neurofibromas not visible on the body surface.
Pain was a feature in 17 of 23 tumours;. increase in size was present in 19 of 19 visible tumours; neurological deficit was present in 14 out of 23 tumours.