Combinations of signs in 206 TAN patients
| Signs | n (%) |
| Two signs: | |
| Sensory polyneuropathy+gait ataxia | 90 (43.7) |
| Sensory polyneuropathy+optic atrophy | 28 (13.6) |
| Sensory polyneuropathy+neurosensory deafness | 2 (1.0) |
| Optic atrophy+neurosensory deafness | 4 (2.0) |
| Three signs: | |
| Sensory polyneuropathy+gait ataxia+optic atrophy | 44 (21.0) |
| Sensory polyneuropathy+gait ataxia+neurosensory deafness | 16 (7.7) |
| Sensory polyneuropathy+optic atrophy+neurosensory deafness | 4 (2.0) |
| All the four signs | 18 (8.7) |