Patient No | Age | Sex | MDRS | Warm up | DS | DL | SS | SL |
---|---|---|---|---|---|---|---|---|
*, † ‡ Patients deriving from the same family. | ||||||||
MDRS, Muscular disability rating scale developed by Mathieu et al.16 MDRS, ordinal scale of clinical muscular impairment ranging from 1 (no impairment) to 5 (severe proximal weakness, confined to wheelchair); yes or no, whether the patient's value exceeds the normal limits computed in the control group. DS and DL, respectively the duration values for small and large target displacements; SS and SL, respectively the skewness values for small and large target displacements. | ||||||||
1 | 47 | F | 3 | Yes | No | Yes | No | No |
2 | 56 | M | 3 | No | No | No | No | No |
3* | 28 | M | 4 | No | Yes | No | No | |
4* | 30 | F | 4 | Yes | Yes | No | Yes | |
5 | 50 | F | 4 | No | No | No | Yes | Yes |
6 | 44 | M | 4 | Yes | Yes | No | Yes | No |
7 | 26 | M | 2 | No | Yes | Yes | No | No |
8 | 58 | F | 4 | Yes | Yes | Yes | Yes | No |
9 | 60 | M | 4 | Yes | Yes | Yes | Yes | No |
10‡ | 27 | M | 3 | Yes | Yes | Yes | Yes | Yes |
11‡ | 21 | F | 3 | Yes | Yes | Yes | Yes | Yes |
12 | 34 | M | 2 | Yes | Yes | Yes | No | No |
13 | 68 | M | 2 | Yes | No | No | No | No |
14 | 57 | F | 4 | Yes | Yes | No | Yes | No |
15 | 15 | F | 3 | Yes | No | No | Yes | No |
16 | 34 | M | 3 | No | Yes | Yes | Yes | No |
17 | 67 | M | 4 | No | No | No | No | No |
18‡ | 49 | F | 2 | Yes | Yes | No | No | Yes |
19‡ | 21 | F | 3 | Yes | Yes | Yes | Yes | Yes |
20 | 35 | F | 4 | Yes | No | No | Yes | No |