Table 2

Summary of evidence

ConditionEvidence level
*Not specifically discussed at one day authors' meeting.
Guillain-Barré syndrome1a
Chronic inflammatory demyelinating polyneuropathy1b
Multifocal motor neuropathy1b
Other lower motor neuron syndromesIV
Amyotrophic lateral sclerosis*III against current use
Neuropathy associated with paraproteinIV
Myasthenia gravis (acute severe or deteriorating)1b
Lambert-Eaton syndrome1b
Inclusion body myositis1b against current use
Dermatomyositis1b
PolymyositisIV
Stiff-man syndromeIII/IV
Multiple sclerosis (relapse rate ?disability)1b
Kawasaki disease1a
Sarcoid, Behçet's diseaseno evidence
CNS vasculitisIII/IV
CNS lupus, antiphospholipid syndromesIV
EpilepsyIII/IV
Lennox Gastaut, West syndromesIII/IV
Rasmussen encephalitisIV
Landau-Kleffner syndromeIV
Paraneoplastic disorders of the CNSIII/IV
Adrenoleukodystrophy*158III against current use