Table 1

Hereditary dementias

DiseaseGeneChromosome
Familial Alzheimer’s diseaseβ-APP 21
PS-114
PS-21
Sporadic Alzheimer’s diseaseApoE19
Hereditary cerebral haemorrhage with amyloidosis of the Dutch typeβ-APP21
Familial Creutzfeldt Jakob diseasePrion20
Familial fatal insomniaPrion20
Gerstmann-Sträussler-ScheinkerPrion20
FTDP-17Tau17
Frontotemporal dementia (Jutland)?3
Frontotemporal dementia?9
Huntington’s diseaseIT-154
CADASILNotch 319
Familial British dementiaBRI213
Familial Danish dementiaBRI213
FENIBPI123