Table 2

Some hereditary diseases that may present with dementia in adulthood

Inheritance
Most of these diseases are discussed elsewhere in this supplement.
AdrenoleukodystrophyX linked
Dentatorubropallidoluysian atrophyAutosomal dominant
Mitochondrial disorders (MERFF, MELAS, Leighs)Maternal
Niemann Pick type CAutosomal recessive
Parkinson’s diseaseAutosomal dominant
Spinocerebellar ataxiaAutosomal Dominant
Wilson’s diseaseAutosomal Recessive