Prevalence of sporadic, idiopathic LOCA (ILOCA) cases in the whole BTHA population (crude and sex specific rates) and prevalence of familial LOCA cases with and without defined genetic loci
| Population (BTHA) | Prevalent cases | Estimated prevalence |
|---|---|---|
| BTHA, Bro Taf Health Authority; LOCA, late onset cerebellar ataxia | ||
| Sporadic, idiopathic LOCA (ILOCA) cases | ||
| Whole (n = 742 400) | 63 | Crude rate 8.4 per 100 000 (95% CI 7.2 to 11.6) |
| Males (all ages) (n = 366 800) | 42 | Sex specific rate 12.5 per 100 000 (95% CI 8.9 to 16.2) |
| Females (all ages) (n = 375 600) | 21 | Sex specific rate 6.4 per 100 000 (95% CI 3.8 to 9.0) |
| Inherited LOCA cases | ||
| Whole (n = 742 400) | 13 | Crude rate 1.8 per 100 000 (95% CI 0.8 to 2.7) |
| Defined genetic cause (n = 742 400) | 6 | Crude rate 0.81 per 100 000 (95% CI 0.1 to 1.5) |
| Undefined genetic cause (n = 742 400) | 7 | Crude rate 0.9 per 100 000 (95% CI 0.2 to 1.6) |