Table 3

 Comparison of contemporary prevalence data of inherited ataxias from several countries for the subgroup of LOCA with genetic basis*

Reference (country)Prevalence rate* (per 100 000)Predicted prevalence rate (per 100 000)
Koeppen et al 197722 (UK)0.310.15 (95% CI 0.03 to 0.27)
Sridharan et al 198527 (Libya)4.82.1 (95% CI 0.8 to 3.42)
Orozco et al 198925 (Cuba)4122.3 (95% CI 15.6 to 29)
Polo et al 199126 (Spain)20.23.3 (95% CI 1.7 to 4.9)
Leone et al 199523 (Italy)14.88.7 (95% CI 3 to 14.4)
Current study1.81.8 (95% CI 0.8 to 2.7)