Table 1

 Clinical profiles of eight patients with pure autonomic failure at their first visit

VariablePatient
12345678
*Normal range 150 to 450 pg/ml.
F, female; M, male; y, years.
SexMMMMMMMF
Onset age (y)3568727850525150
Time until first evaluation (y)171105277513
Duration of observation (y)327121232141529
Hypohidrosis++++++++
Faintness++++++++
Syncope++++
Constipation+++
Difficulty in urination++
Incontinence/urinary urgency+++
Respiratory disturbance
Plasma noradrenaline (pg/ml) *3043258350341410
Orthostatic hypotension++++++++
Denervation supersensitivity++++++++
Modified Rankin scale00000000