Table 2

 Responses of and outcomes for 15 CIDP patients after treatment with the proposed standardised protocol

PatientAge at onset/sexInitial therapy and responseMaintenance therapies and responsesOutcomes*NIS (severe side)†
1234Before treatmentAfter stabilisation and remission
*Duration of remission since steroids were stopped.
†Neurological impairment score; previously called the neurological disability score (described by Dyck PJ et al2); sum score of maximum severity = 120.
‡Patient in case report.
IVIg, intravenous immunoglobulin.
1‡34/MPlasma exchangeOral prednisoloneCyclophosphamide pulseCiclosporinStabilised for 26 months510
Temporarily respondedTemporarily responded, relapsed during taperingUnchangedResponded
247/MPlasma exchangeOral prednisoloneNo therapy requiredComplete remission420
Temporarily respondedResponded(40 months)
359/FPlasma exchangeOral prednisoloneNo therapy requiredComplete remission390
Temporarily respondedResponded(34 months)
462/MPlasma exchangeOral prednisoloneNo therapy requiredComplete remission670
Temporarily respondedResponded(32 months)
546/MIVIgOral prednisoloneNo therapy requiredComplete remission360
Rapidly respondedResponded(29 months)
652/MIVIgOral prednisoloneNo therapy requiredComplete remission280
Rapidly respondedResponded(28 months)
744/FIVIgOral prednisoloneNo therapy requiredComplete remission460
Slowly respondedResponded(24 months)
811/MIVIgOral prednisoloneNo therapy requiredComplete remission300
Rapidly respondedResponded(18 months)
953/MIVIgOral prednisoloneCyclophosphamide pulseCiclosporinTacrolimusStabilised for 12 months;6612
Temporarily respondedUnchanged, relapsed during taperingUnchangedUnchangedUnchangedmaintained IVIg
1045/FIVIgOral prednisoloneCiclosporinStabilised for 9 months;376
Temporarily respondedTemporarily responded, relapsed during taperingRespondedmaintained IVIg; no further relapses
1134/FIVIgOral prednisoloneCiclosporinStabilised for 20 months;457
Temporarily respondedTemporarily responded, relapsed during taperingRespondedno IVIg required; no further relapses
1265/FIVIgOral prednisoloneCiclosporinStabilised for 18 months;484
Temporarily respondedUnchanged, progressedRespondedno IVIg required; no further relapses
1319/FIVIgOral prednisoloneStabilised for 12 months;314
Rapidly respondedRespondedno IVIg required
1445/MIVIgOral prednisoloneStabilised for 11 months;426
Rapidly respondedRespondedno IVIg required
1537/MIVIgOral prednisoloneStabilised for 6 months;373
Rapidly respondedRespondedno IVIg required