Table 1

 Clinical features

NP definiteNP probable
MRC, Medical Research Council; NP, neurophysiologically; ODSS, Overall Disability Sum Score.
n (%)27 (54)23 (46)
Patients who responded to treatment, n (%)20 (74)17 (73.9)
Male/female13/1418/5
Mean (range) age at assessment, years54.2 (14–81)53.7 (17–76)
Mean (SD) duration of disease, years7.7 (6.8)9.89 (9)
Mean (SD) MRC score at initiation of treatment57.8 (10)53.7 (14)
Mean (SD) ODSS score at initiation of treatment6.3 (1.8)6.1 (2.9)
Symmetrical sensorimotor phenotype, n (%)16 (59.3)14 (60.9)
ASSM phenotype, n (%)3 (11.1)5 (21.7)
DSSM phenotype, n (%)5 (18.5)4 (17.4)
Symmetrical motor phenotype, n (%)1 (3.7)0
Symmetrical sensory phenotype, n (%)2 (7.4)0
Patients who had CSF analysis, n (%)24 (88.9)18 (78.3)
Patients with CSF protein>400 mg/l, n (%)19 (79.2)16 (88.9)
Patients who had nerve biopsy, n (%)16 (59.3)11 (47.8)
Patients who had pathological lymphocytic endoneurial infiltrates, n50
Patients who had pathological numbers of demyelinated/remyelinated fibres, n76