Published individual outcome data on patients with heredodegenerative forms of dystonia operated on with deep brain stimulation
| Heredodegenerative | Individual patient data | Age at surgery, mean (SD) | Duration of symptoms, mean (SD) | Preop Severity score, mean (SD) | Percentage improvement in motor/severity score following deep brain stimulation, mean (SD) IQR | References |
| Pantothenate kinase associated neurodegeneration | 12 | 21.9 (12.2) | 11.2 (7.6) | 74.9 (29.7) | 66 (21.9) 56.3–81.2 | 26 31 47 87–90 |
| Lubag X linked dystonia parkinsonism | 2 | 39.5 (7.8) | 7.5 (9.2) | 58.8 (26.5) | 78 | 91 92 |
| Lesch–Nyhan | 1 | 16 | 15 | 90 | 44 | 93 |
| Dystonia deafness | 1 | 29 | 5 | 53 | 75 | 94 |
| GM1 gangliosidosis | 1 | 24 | 8 | 70 | 20 | 95 |
| Rapid-onset dystonia parkinsonism | 2 | 23.5 (0.7) | 7 (7.1) | 52.8 (3.9) | 13 | 96 97 |