Table 1

NIV data set: descriptive statistics

Total casesn=128
Site of onsetBulbar 32 (25%)Limb 96 (75%)
GenderFemale 37 (29%)Male 91 (71%)
Age at symptom onset (years)Median 57.0IQR 50–64
Range 22–76
Diagnostic delay (months)Median 10.3IQR 6.0–15.0
Range 1.0–55.1
Riluzole useYes 32 (25%)No 96 (75%)
Survival from NIV initiation (months)Median 5.7IQR 2.1–11.3
Range 0.1–38.9
  • NIV, non-invasive ventilation.