Table 2

SEALS data set: descriptive statistics

Total casesn=575
Site of onsetBulbar 189 (33%)Limb 386 (67%)
GenderFemale 239 (42%)Male 336 (58%)
Age at symptom onset (years)Median 61.5IQR 54–69
Range 23–89
Diagnostic delay (months)Median 11.1IQR 7.0–19.0
Range 1.0–296
Riluzole useYes 260 (45%)No 315 (55%)
Survival from diagnosis (months)Median 17.7IQR 8.3–29.9
Range 0.6–268
  • SEALS, South-East England register for amyotrophic lateral sclerosis.