Table 1

Clinical classification of patients with and without ALS

FTD only (N=611)ALS/FTD (N=89)χ2p Value
N (%)N (%)
bvFTD307 (50.2)70 (78.7)25.22<0.001***
SD90 (14.7)3 (3.4)8.700.004**
PNFA111 (18.2)1 (1.1)16.79<0.001***
bvFTD/SD70 (11.5)10 (11.2)0.0041.00
bvFTD/PNFA31 (5.1)5 (5.6)0.0471.00
bvFTD/SD/PNFA†2 (0.3)0 (0)1.00
  • **p<0.01 ***p<0.001.

  • †Fisher’s exact statistic used as expected cell counts below 5.

  • ALS, amyotrophic lateral sclerosis; bvFTD, behavioural form of FTD; FTD, frontotemporal dementia; PNFA, progressive non-fluent aphasia; SD, semantic dementia.