Summary
A 73-year-old woman without liver cirrhosis developed choreoathetoid movements of the limbs due to portal-systemic encephalopathy. A prominent spleno-renal shunt was demonstrated by non-invasive methods (abdominal computed tomography and sonography) as well as arterial portography. The choreoathetoid movements were improved by a protein-resticted diet and administration of lactulose. A portal systemic shunt should be considered when investigating choreoathetosis, even in patients without liver cirrhosis.
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Yokota, T., Tsuchiya, K., Umetani, K. et al. Choreoathetoid movements associated with a spleno-renal shunt. J Neurol 235, 487–488 (1988). https://doi.org/10.1007/BF00314253
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DOI: https://doi.org/10.1007/BF00314253