Summary
CT has been performed in five patients affected by amyotrophic choreo-acanthocytosis (ACA) and bicaudate diameter, bicaudate index and frontal horn/bicaudate ratio (FH/CC) have been evaluated. Findings have been confirmatory of caudate nuclei atrophy as shown by previous ACA autopsy reports, but did not differ from Huntington's chorea CT picture. There was no correlation between CT measurements and age, illness duration or degree of hyperkinesia in contradistinction to that reported for Huntington's chorea.
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References
Sax DS, Menzer L (1977) Computerized tomography in Huntington disease. Neurology 27: 388
Barr AN, Heinze WJ, Dobben GD, Valvassori GE, Sugar O (1978) Bicaudate index in computerized tomography of Huntington disease and cerebral atrophy. Neurology 28: 1196–1200
Stober T, Wussow W, Schimrigk K (1984) Bicaudate diameter: the most specific and simple CT parameter in the diagnosis of Huntington's disease. Neuroradiology 26: 25–28
Serra S, Xerra A, Arena A (1986) Amyotrophic choreo-acanthocytosis: a new observation in Southern Europe. Acta Neurol Scand 73: 481–485
Bird TD, Cederbaum S, Valpey RW, Sthal WL (1978) Familial degeneration of the basal ganglia with acanthocytosis: a clinical, neuropathological, and neurochemical study. Ann Neurol 3: 253–258
Sato Y, Ohnishi A, Tateishi J (1984) An autopsy case of chorea-acanthocytosis: special references to the histopathological and biochemical findings of basal ganglia. Brain Nerve (Japan) 36: 105–111
Lang C (1985) Is direct CT caudatometry superior to indirect parameters in confirming Huntington's disease? Neuroradiology 27:161–163
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Serra, S., Xerra, A., Scribano, E. et al. Computerized tomography in amyotrophic choreo-acanthocytosis. Neuroradiology 29, 480–482 (1987). https://doi.org/10.1007/BF00341748
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DOI: https://doi.org/10.1007/BF00341748