Main articleCentral motor conduction in Hirayama disease
References (9)
Contribution of human reflex study to understanding and management of pyramidal syndrome
- et al.
H reflex studies in neurolathyrism
Electroenceph. clin. Neurophysiol.
(1994) - et al.
Multifocal motor neuropathy
Juvenile non-progressive muscular atrophy localised to hand and forearm — observation in 3 cases
Clin. Neurol.
(1972)
Cited by (60)
Establishment of a clinician-led guideline on the diagnosis and treatment of Hirayama disease using a modified Delphi technique
2020, Clinical NeurophysiologyCitation Excerpt :Therefore, HD is primarily a lower motor neuron (LMN) disease that may be another possibility. Although some previous studies demonstrated that HD patients with long disease duration may develop cervical cord injury with disease progression (Misra and Kalita, 1995; Zheng et al., 2017c), most panelist considered the pyramidal tract signs do not exist in the majority of HD patients since more studies, especially the previous autopsy studies, confirm that HD is a disorder involving lesion of LMN (Hirayama et al., 1987; Hirayama, 2000b; Lyu et al., 2011). Therefore, if patients who have been diagnosed as HD through clinical features and auxiliary examinations listed in this expert-led guideline presented with pyramidal tract signs, regular follow-up is suggested to rule out the possibility of motor neuron disease (statement #11, Level V).
A Confirmed Case in the United Kingdom of Hirayama Disease in a Young White Male Presenting with Hand Weakness
2017, World NeurosurgeryCitation Excerpt :In more than 30% of patients, there may be bilateral but asymmetric involvement, and the clinical course usually stabilizes after a period of progression, with the disease reaching a stationary phase by 5 years in around 95% of patients.1 Hirayama disease is usually a sporadic disorder, and is predominantly a disease found in Asian countries.1-12 In contrast, fewer cases have been reported in Europe,13-32 North America,33-37 and Australia.38
Cortical function and corticomotoneuronal adaptation in monomelic amyotrophy
2017, Clinical NeurophysiologyCitation Excerpt :Previous studies using single-pulse TMS have reported inconsistent changes in monomelic amyotrophy patients. Specifically, these studies have described decreased or increased MEP amplitude and prolongation of CMCT though the upper and lower limbs with the neck in standard and flexed positions respectively, supporting the hypothesis of a cervical flexion myelopathy (Imai et al., 2000; Pal et al., 2008 Shizukawa et al., 1994; Misra and Kalita, 1995). In contrast, others studies have determined normal CMCT values independent of neck position (Khandelwal et al., 2004; Abraham et al., 2013; Boelmans et al., 2013).
Benign focal amyotrophy
2017, Revue NeurologiqueCitation Excerpt :Fasciculations may be observed in about one-quarter of patients [58]. The amyotrophy may extend to the contralateral leg, but always asymmetrically, especially in distal forms [16–57]. Nerve conduction studies are normal except for reduced CMAP amplitudes in the common peroneal nerve in some patients.
A study of dynamic F-waves in juvenile spinal muscular atrophy of the distal upper extremity (Hirayama disease)
2016, Journal of the Neurological SciencesEffect of neck flexion on somatosensory and motor evoked potentials in Hirayama disease
2013, Journal of the Neurological Sciences