Abstract
The case of a young woman suffering from a rare cerebrovascular disease associated with livedo reticularis (Sneddon syndrome) is reported. Hemicranic attacks were the first symptom detected. The patient had a progressive clinical course of neurologic symptoms. Cerebral CT scan, NMR and cerebral arteriography revealed a progressive cerebral multifarctual feature involving middle-size arteries.
MeSH terms
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Adult
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Arterial Occlusive Diseases / diagnosis
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Arterial Occlusive Diseases / genetics*
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Cerebral Infarction / diagnosis
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Cerebral Infarction / genetics
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Cerebrovascular Disorders / diagnosis
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Cerebrovascular Disorders / genetics*
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Chromosome Aberrations / diagnosis
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Chromosome Aberrations / genetics*
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Chromosome Disorders
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Female
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Frontal Lobe / blood supply
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Genes, Dominant / genetics*
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Humans
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Magnetic Resonance Imaging
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Migraine Disorders / diagnosis
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Migraine Disorders / genetics*
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Skin / blood supply*
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Syndrome