CT and MR imaging of Susac syndrome in a young male presenting with acute disorientation

Andrew M Allmendinger; Vadim Spektor; Sylvie Destian

doi:10.1016/j.clinimag.2009.09.003

CT and MR imaging of Susac syndrome in a young male presenting with acute disorientation

Clin Imaging. 2010 Mar-Apr;34(2):138-42. doi: 10.1016/j.clinimag.2009.09.003.

Authors

Andrew M Allmendinger¹, Vadim Spektor, Sylvie Destian

Affiliation

¹ St. Vincent's Catholic Medical Center, 170 W 12th St., New York, NY 10011, USA. amallmendinger@gmail.com

PMID: 20189079
DOI: 10.1016/j.clinimag.2009.09.003

Abstract

Susac syndrome is a rare neurologic disorder first described by Susac et al. in 1979. Clinically, Susac syndrome consists of a triad including encephalopathy, branch retinal artery occlusion, and sensorineural hearing loss. Microinfarction is believed to be the basic histologic feature and MR is considered the best imaging modality. This case documents the typical imaging findings of Susac syndrome, as well as the unique MR imaging finding of cranial nerve enhancement.

Publication types

Case Reports

MeSH terms

Acute Disease
Adult
Brain / diagnostic imaging*
Brain / pathology*
Confusion / diagnosis*
Diffusion Magnetic Resonance Imaging / methods*
Humans
Male
Susac Syndrome / diagnosis*
Tomography, X-Ray Computed / methods*