A case of central neurocytoma is reported, presenting as a tumor of the occipital lobe, closely related to the ependyma of the occipital horn of the lateral ventricle but not actually invading it. This is a distinctly uncommon location, and only four tumors have been reported so far in a lobar position, without an intraventricular component. The case broadens our knowledge of this recently described tumor and gives an opportunity for discussion of the role of radiotherapy in its management, which currently remains controversial.