Head and neck paragangliomas are tumors arising from specialized neural crest cells.
Prominent locations are the carotid body along with the vagal, jugular, and tympanic glomus …

Understanding of molecular mechanisms of tumor growth has an increasing impact on the
development of diagnostics and targeted therapy of human neoplasia. In this review, we …

OBJECTIVE: Hemangioblastomas are benign vascular tumors of the central nervous system.
Several cases of spontaneous hemorrhage within these tumors have been reported …

OBJECTIVES Haemangioblastoma of the CNS occurs as a sporadic entity and as a
manifestation of the autosomal dominant von Hippel-Lindau disease with the major …

Hemangioblastomas are central nervous system (CNS) tumors of unknown histogenesis,
which can occur sporadically or in von Hippel-Lindau disease. Hemangioblastomas are …

OBJECTIVE: Hemangioblastomas of the central nervous system are rare vascular tumors
that can occur as sporadic lesions or as component tumors of autosomal dominant von …

Abstract Context: McCune-Albright syndrome (MAS) is caused by sporadic mutations of the
GNAS. Patients exhibit features of acromegaly. In most patients, GH-secreting pituitary …

Background: The role of autosomal dominant polycystic kidney disease (ADPKD) as a risk
factor for renal cell carcinoma (RCC) is still under discussion. Data on prevalence of RCC in …

This review focuses on CNS hemangioblastomas in von Hippel–Lindau (VHL) disease. The
pathogenesis of these lesions remains unclear to date; however, biallelic inactivation of the …

Sporadic and hereditary forms of renal cell carcinoma (RCC), von Hippel–Lindau (VHL)
disease and the familial paraganglioma syndromes are closely related in terms of their …