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A case of progressive subcortical gliosis presenting clinically as Steele-Richardson-Olszewski syndrome.
  1. R G Will,
  2. A J Lees,
  3. W Gibb,
  4. R O Barnard
  1. Maida Vale Hospital for Nervous Diseases, London, UK.


    A patient presenting with the characteristic clinical features of Steele-Richardson-Olszewski syndrome is described, in whom neuropathological examination revealed atypical features, including extensive cortical and subcortical gliosis. The clinical and pathological features are discussed with particular reference to Creutzfeldt-Jacob disease and it is proposed that the case should be classified as progressive subcortical gliosis.

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