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Arnold-Chiari malformation type I (ACM I) is a developmental anomaly of the rhombencephalon characterised by displacement of the cerebellar tonsils into the foramen magnum and elongation of the medulla. It usually presents in adult life with head motion induced oscillopsia, ataxia, headaches, cervical pain, or Valsalva induced dizziness.1
Various ocular motor abnormalities have been reported in patients with ACM I. Among these, downbeat nystagmus and periodic alternating nystagmus are the most common. Other often encountered ocular signs, such as gaze evoked nystagmus, rebound nystagmus, and impaired smooth pursuit, reflect cerebellar involvement.2 3
Vertigo of vestibular origin, being peripheral or central, is usually accompanied by nystagmus and nausea, or vomiting, and is often influenced by head position.3 4 The entity of central positioning vomiting without, or little, vertigo and nystagmus (posturally evoked vomiting (PEV)) was first reported by Drachmanet al and later recognised by Brandt and Baloh and Halmagyi.3-5
Posturally evoked vomiting is generally poorly known as a warning symptom of a posterior fossa lesion and is often misinterpreted.5 Whereas it has been documented in patients with posterior fossa tumours, it has not been reported in patients with developmental abnormalities. We report on a patient with ACM I where PEV was the most prominent presenting symptom.
This 57 year old woman was seen in …
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