A 23-year-old woman visited the outpatient clinic for recently aggravating headache, limb weakness, hypesthesia, gait disturbance, diplopia, right hearing loss and dysarthria. Neurological symptoms had begun with right arm weakness 4 years previously. Cerebrovascular lesion had been diagnosed at the other hospital without subsequent treatment.

On examination, there was haemangioma on the right side of the face and tongue which was said to exist from birth …