An 85 year old man presented with a 6 month history of progressive proximal muscle weakness, with associated paraesthesia, and dysphagia. Clinical examination showed signs of a peripheral neuropathy, proximal muscle wasting, and weakness of the lower limbs. Electrophysiological examination demonstrated a generalised axonal sensori-motor neuropathy, with a superimposed proximal myopathy. Creatinine kinase concentration and erythrocyte sedimentation rate …