RT Journal Article SR Electronic T1 Isolated myoclonic alien hand as the sole presentation of pathologically established Creutzfeldt-Jakob disease: a report of two patients JF Journal of Neurology, Neurosurgery & Psychiatry JO J Neurol Neurosurg Psychiatry FD BMJ Publishing Group Ltd SP 404 OP 407 DO 10.1136/jnnp.63.3.404 VO 63 IS 3 A1 D J L MacGowan A1 N Delanty A1 F Petito A1 M Edgar A1 J Mastrianni A1 S J DeArmond YR 1997 UL http://jnnp.bmj.com/content/63/3/404.abstract AB Creutzfeldt-Jakob disease may have many atypical presentations before the development of classic progressive dementia and startle myoclonus. In two patients with pathologically established disease association with a progressive alien hand syndrome was the sole initial manifestation of the disease.