PT  - JOURNAL ARTICLE
AU  - CA Abela
AU  - L Mclellan
AU  - K Truscott
AU  - O Jeelani
AU  - D Dunaway
AU  - J Britto
AU  - R Hayward
AU  - B Jones
AU  - Z Diwan
TI  - A 10 YEAR EXPERIENCE OF OVER 100 FRONTOFACIAL PROCEDURES IN SYNDROMIC CHILDREN AND THEIR COMPLICATIONS
AID  - 10.1136/jnnp-2012-304200a.22
DP  - 2012 Nov 01
TA  - Journal of Neurology, Neurosurgery & Psychiatry
PG  - A5--A6
VI  - 83
IP  - Suppl 2
4099  - http://jnnp.bmj.com/content/83/Suppl_2/A5.3.short
4100  - http://jnnp.bmj.com/content/83/Suppl_2/A5.3.full
SO  - J Neurol Neurosurg Psychiatry2012 Nov 01; 83
AB  - Complex craniofacial procedures form a distinct subgroup of transcranial or frontofacial surgery. The paediatric population undergoing these procedures mainly include the syndromic dysostoses, central facial hypoplasias or clefts and cranio-fronto-nasal dysplasia. We reviewed the case notes, hospital electronic records, logbooks and departmental database to review the series of frontofacial cases over the last 10 years. We collated demographic data, clinical diagnoses, operative records and episodic details. The unit has performed 105 frontofacial surgical procedures in children with Apert, Crouzon, Pfeiffer and other Syndromes. Within this population, it has been necessary to perform monobloc distractions, facial bipartition distractions, box osteotomies and facial bipartitions without distraction, as well as 2 Le Fort 3 advancements in combination with Fronto-orbital remodelling. During this period we have recorded 58 complications. From the patients that were investigated, there was a 9% major complication rate and 4% revision rate. Bipartition and box osteotomy procedures are significantly safer than distraction procedures. Overall, the main findings were as follows: • Peri-operative mortality rate 1% • Relapse rate 2% • Peri-operative massive transfusion risk 5% • Post-operative epilepsy for distraction 5% • Frontofacial surgery is comparable to other complex major surgeries • Distraction increases complication rate and doubles hospital stay but is still safe.