Table 1

Patient characteristics and their clinical and electrophysiological findings

Patient NoSexAge (y)UMNSBSNorris score (%)Frenchay test (%)SAMUAP analysisPeak ratio analysis
Limb onset
1F58++5588SPNGNG
2M73+5497SPNGN
3F64+6195UNGN
4F52++8286SPNGN
5M70+7091UNN
6F49+7798UNN
7M64+7689SPNN
8F52+85100SPNGN
9F69++4573SPNGN
10M55++8388UNGNG
Bulbar onset
11F55++8577SPNNG
12M69++5414SPNGNG
13F75++6972UNGNG
14M68++8738SPNGNG
15M62+857UNGNG
16F72++8863SPNNG
17M57++4623SPNGNG
18M52++5230UNGNG
  • UMNS = Upper motor neuron signs; BS = bulbar signs; SA = spontaneous activity (fibrillations, or fasciculations, or repetitive discharges); SP = definitely present; NG = neurogenic; N=normal.