Age at onset and clinical features of family 184
Subject | Age (y) at onset | Age (y) at death | Age (y) when assessed | Duration of illness (y) | ApoE genotype | First symptom | Other symptoms | Psychiatric features | Neurological features | Seizures |
---|---|---|---|---|---|---|---|---|---|---|
184.I.1 | — | 58 | — | — | — | — | — | — | — | |
184.II.1 | 51 | 66 | — | 15 | — | — | — | — | — | |
184.II.2 | — | Early 60s | — | — | — | — | — | — | ||
184.III.1 | 55 | 69 | — | 14 | — | — | — | — | — | |
184.III.3 | 56 | — | 60 | > 7 | 3,4 | Loss of confidence | Visual agnosia, language impairment | Visual hallucinations, depression | Myoclonus | 0 |
184.III.4 | 49 | 55 | — | 6 | — | Memory | Visual agnosia, language impairment | 0 | Myoclonus, supranuclear opthalmoplegia, extrapyramidal signs | 0 |
184.III.5 | 50 | — | 56 | 6+ | — | Memory | Language impairment | Visual hallucinations, depression | 0 | 0 |
+ = Present; — = unknown; 0 = absent.