Table 1

 Age at onset and clinical features of family 184

SubjectAge (y) at onsetAge (y) at deathAge (y) when assessedDuration of illness (y)ApoE genotypeFirst symptomOther symptomsPsychiatric featuresNeurological featuresSeizures
184.I.158
184.II.1516615
184.II.2Early 60s
184.III.1556914
184.III.35660> 73,4Loss of confidenceVisual agnosia, language impairmentVisual hallucinations, depressionMyoclonus0
184.III.449556MemoryVisual agnosia, language impairment0Myoclonus, supranuclear opthalmoplegia, extrapyramidal signs0
184.III.550566+MemoryLanguage impairmentVisual hallucinations, depression00
  • + = Present; — = unknown; 0 = absent.