Brain stem auditory evoked potentials in this patient show marked delay of wave I latencies with preservation of interwave I–V latencies compared with laboratory controls
| Latency (ms) | Normal range Mean (SD) | HMSN 1A ( n=1) | |||
|---|---|---|---|---|---|
| Left | Right | ||||
| Wave I | 1.7 (0.15) | 2.22 | 2.37 | ||
| Wave IV | 5.1 (0.24) | 6.30 | 6.33 | ||
| Wave V | 5.7 (0.25) | 6.60 | 6.68 | ||
| Interwave I–V | 4.0 (0.23) | 4.38 | 4.31 | ||