Mean age at hearing loss and interval between diagnosis in sporadic and familial cases
| M/F | Age (y) HL | Age (y) VS | FU (y) | Interval 1st to 2nd | Mutation detected Yes/No | |||||
|---|---|---|---|---|---|---|---|---|---|---|
| Mean (range) | ||||||||||
| Sporadic: | ||||||||||
| UVS | 6/13 | 31.2 | 34.4 | 4.2 | — | 5/11 | ||||
| (S1–19) | (15–57) | (15–59) | (1–15) | |||||||
| BVS | 4/9 | 21.6 | 25.1 | 12.9 | 6.4 | 2/9 | ||||
| (S20–32) | (6–44) | (11–48) | (4–29) | (0–22) | ||||||
| Familial: | ||||||||||
| BVS | ||||||||||
| Parent | 4/2 | 27.8 | 37.0 | 12.8 | 6.5 | 5/1 | ||||
| (P1–6) | (17–37) | (18–56) | (6–21) | (0–16) | ||||||
| Child | 2/3 | 16.0 | 17.6 | 6.0 | 3.8 | 2/3 | ||||
| (C3–7) | (13–21) | (11–27) | (5–7) | (2–6) | ||||||
| UVS: | ||||||||||
| Child | 1/1 | 24 | 23.5 | 3.5 | — | 2/0 | ||||
| (C1–2) | (19–29) | (18–29) | (3–4) | |||||||