Presenting symptoms or signs in 122 Swedish patients with CJD 1985-96. Most common combination of symptoms and signs was dementia and ataxia (17 patients)
| Symptom/sign | n |
|---|---|
| Dementia | 61 |
| Ataxia/vertigo | 48 |
| Aphasia/apraxia | 10 |
| Paresis of extremities | 7 |
| Depression | 6 |
| Sensory | 4 |
| Oculomotor | 3 |
| Rigidity/tremor | 3 |
| Visual | 2 |
| Myoclonus | 2 |