Summary of pathological findings in the two cases
| Case 1 | Case 2 | |
| Macroscopic | ||
| Posterior frontal lobe (BA 6,8) atrophy | +++ | +++ |
| Frontal pole atrophy | + | + |
| Precentral gyrus atrophy | + | ± |
| Anterior cingulate gyrus atrophy | +++ | ++ |
| Temporal pole atrophy | ++ | ++ |
| Parahippocampal gyrus atrophy | ++ | + |
| Hippocampal formation atrophy | ± | ± |
| Parietal lobe atrophy | + | + |
| Occipital lobe atrophy | + | − |
| Substantia nigra depigmentation and atrophy | +++ | +++ |
| Caudate atrophy | ++ | + |
| Pallidal atrophy | + | + |
| Thalamic atrophy | − | − |
| Subthalamic nucleus atrophy | − | − |
| Microscopic | ||
| Ballooned achromatic neurons | +++ | +++ |
| Tau+ve cytoplasmic neuronal inclusions2-150 | ++ | ++ |
| Glial cytoplasmic inclusions | ++ | ++ |
| Basophilic neuronal cytoplasmic inclusions2-151 | + | +++ |
| Pale body neuronal cytoplasmic inclusions2-151 | ++ | ++ |