Table 1

Characteristics of patients

AgeSexYears from diagnosisSide of affected eyeWorst documented visual acuityBrain MRIAcuity on day of studyColour vision on day of studyMRI optic nervesVEP latency at presentation (ms)VEP latency at follow up (ms)
RLRLAffectedUnaffectedAffectedUnaffected
38F14R6/9Normal6/56/517/1717/17Abnormal (R)119.0108.0101.1 97.1
49M13L6/36Normal6/56/517/1716/17Normal114.0112.5103.1101.6
31M0.5L6/18Normal6/5-26/5-217/1715/17Abnormal (L)NDND121.5102.6
33F12L6/60Normal6/46/416/1715/17Abnormal (L)147.0106.0 99.6 98.6
35M3L6/24Normal6/5-26/616/1715/17Abnormal (L)NDND118.6103.3
34M1LNPLNormal6/46/517/1716/17NormalNDND 97.2 96.2
45F12LCFNormal6/56/517/1715/17Abnormal (L)No pattern107.0 98.1 96.6
  • NPL=No perception of light; CF=counting fingers; ND=not done; acuity=smallest type seen on the Snellen chart; colour vision=number of Ishihara plates correctly identified.