Table 1

Neuronal counts (/mm2) with and without nuclear inclusions

CaseAge at onset/death (years)SexInclusions present (n/mm2)Inclusions absent (n/mm2)Total
*Significantly smaller than the control group (p < 0.01; Mann–Whitney U test).
F, female; M, male; SCA1, spinocerebeller ataxia type 1.
SCA1 case 139/55F247195
SCA1 case 241/50M296796
SCA1 case 341/55F326294
SCA1 case 430/50F236790
SCA1 case 546/63F144054
SCA1 case 637/48M234972
SCA1 case 746/66M127486
Mean83.9*
Control/25M0140140
Control/25F0174174
Control/40F0154154
Control/44M0157157
Control/45F0176176
Mean160.2