Table 1

Clinical features in nine patients with amyotrophic lateral sclerosis and neck extensor weakness

Features in addition to head drop
UMN+LMN
NoAge (years)SexInvolvement at onsetInterval to development of head dropNeck flexorsBulbarTongueRelease reflexesJaw jerkULLLDuration of illness at last follow up
F, female; LL, lower limb; LMN, lower motor neurone; Ls, limbs; m, month; M, male; mw, mild weakness; RUL, right upper limb; UL, upper limb; UMN, upper motor neurone; y, year.
155MRUL2 y++++++2 y 6 m
235F4 Ls9 m+++++1 y
364FDysarthria3 y 9 m+++++4 y
450MUL5 mmw++++++1 y
542M4 Ls8 ymw+++++9 y
662MLL8 mmw++++++1 y
765MRUL1 y 9 mmw++++++2 y
849FRUL3 y 9 m+++4 y
958MLL3 mmw+++++2 y